Congenital leukemia is a very rare disorder mostly seen in the first few months with its signs and symptoms also seen in acute non-lymphocytic leukemia form. It accounts for 1% of all leukemias in the first year. Here we to present 48-day-old with late diagnosis of leukemia whose symptoms started by two weeks of age. Anahtar Kelimeler : konjenital lösemi, akut non-lenfoblastik lösemi,congenital Leukemia, acute nonlymphoblastic leukemia.