Wolff-Parkinson-White (WPW) syndrome presents with paroxysmal supraventricular tachycardia and ECG findings of short PR interval with delta wave. Sudden cardiac death can be the first symptom. Analysis of data of 45 patients aged ≤10 years who underwent electrophysiological evaluation for WPW was performed. Thirty-three patients presented with tachycardia and four with syncope; eight were asymptomatic. Atrial fibrillation was induced in six patients, and it degenerated to ventricular fibrillation (VF) in two (1 of these patients was asymptomatic and the other had syncope); accessory pathway effective refractory period was ≤180 ms in both. Ablation was performed in 30 patients; the success rate was 90% (27/30) and recurrence rate was 17% (5/30). Induction of VF in two patients suggests that the prognosis of WPW in early childhood is not without risk. All patients with WPW pattern should be assessed electrophysiologically and risk-stratified. Ablation in patients with risk factors can prevent sudden death.

Keywords: Wolff-Parkinson-White, atriyal fibrilasyon, ventriküler fibrilasyon, supraventriküler taşikardi.