Juvenile xanthogranuloma (JXG) is a rare, benign, non-Langerhans cell histiocytosis of infancy and early childhood characterized by solitary or multiple yellowish cutaneous nodules. The most common sites of these lesions are the head and neck, followed by the upper limbs. In the vast majority of children, JXG is limited to the skin and requires no treatment. The etiopathogenesis is unclear, and the diagnosis is made based on histopathological findings. The patient’s general health is not impaired, and in the absence of associated conditions, the prognosis is excellent. We report three children who presented with solitary and/or multiple nodules diagnosed as JXG together with a review of the literature.

Keywords: jüvenil ksantogranülom, histiyositoz.