The scimitar syndrome is a rare congenital cardiopulmonary anomaly that consists in part of total or partial anomalous venous drainage of the right lung to the inferior vena cava (IVC), lung hypoplasia and anomalous systemic arterial supply to the lung. We present four pediatric patients with different clinical findings.

Keywords: scimitar sendromu, dekstrokardi, akciğer hipoplazisi.