Neuroenteric cysts are rare congenital lesions and they appear due to defect in leaving of notocord from foregut. A definitive diagnosis is made by histopathological examination. Here is a case of a neonate with neuroenteric cyst that is presented by both the thoracic and spinal canal component. Spinal canal component of the neuroenteric cysts must not be forgotten, if there is a suspicion of posterior mediastinal neuroenteric cysts in prenatal ultrasonographic examination. In the diagnosis and treatment of neuroenteric cyst, radiology, surgery, pathology, and neonatology disciplines have to work together.

Keywords: neuroenteric cyst, prenatal diagnosis, newborn