Kaposi sarcoma (KS) is a rare soft tissue tumor. The objective of this study was to report our institutional experience with KS over a 30-year period. From 1990 to 2024, nine children with KS were evaluated. There were 4 males, 5 females. Median age was 10 (3–16) years. Presentation symptoms were nodules and plaques on the skin in 6 patients, and on gingiva in one. One patient was admitted with cervical lymphadenopathy. One patient had fever and hepatosplenomegaly in addition to multiple lymphadenopathies. Post-transplant and classical KS were determined in four cases each, and endemic form was determined in one. Only surgery was performed in 2 patients, post-surgery immunosuppressive therapy dose reduction, interferon alpha and chemotherapy treatments were given to the other patients. Fiveyear overall and event free survival rates were 83.5% and 35.6%. There is no established consensus on treatment of KS in children. Although recurrence was frequent overall survival rate was high in our series. We emphasize that no patient died due to KS in our series. Kaposi sarcoma is a chronic but manageable disease in children.

Keywords: childhood, Kaposi sarcoma, soft tissue tumor