In this study, we analyzed the clinical findings, etiologies, treatments and prognosis of 16 children with posthepatic portal hypertension who were followed in the Department of Pediatric Gastroenterology Hepatology-Nutrition and Liver Transplantation Center of Ege University. Ages of patients were between 1-17 years (Female/Male: 9/7, mean age 10.8 years). Biochemical, histopathological, hematological, and serologic results, and ultrasonographic, endoscopic, cardiologic and angiographic findings were reviewed in all patients. Ascites was found in 13 patients (85%). In this study, the most common reasons for portal hypertension, in order of frequency, were Budd-Chiari syndrome (50%), complication of liver transplantation (31%), constrictive pericarditis (13%) and congenital vena cava obstruction (0.6%). Hypoalbuminemia and hyponatremia were the most serious biochemical findings. Histopathological findings of all patients except those with liver transplantation were compatible with early and advanced stages of cirrhosis.

Keywords: posthepatik portal hipertansiyon, Budd-Chiari sendromu, etiyoloji, prognoz, posthepatic portal hypertension, Budd-Chiari syndrome, etiology, prognosis